{"artifact":{"id":"experiment-exp-wiki-experiments-prion-strain-selective-vulnerability","artifact_type":"experiment","entity_ids":null,"title":"Prion Strain Diversity and Selective Vulnerability","quality_score":0.675,"created_by":"crosslink-v2","provenance_chain":null,"content_hash":null,"metadata":{"source":{"type":"manual","source_name":"wiki","extracted_by":"backfill_v1","extraction_date":"2026-04-16T01:00:16.899018Z"},"summary":"# Prion Strain Diversity and Selective Vulnerability\n## Background and Rationale\nPrion diseases represent a unique category of neurodegenerative disorders characterized by the misfolding and aggregation of the prion protein (PrP), leading to progressive neurodegeneration. Recent evidence suggests that prion-like mechanisms may contribute to Alzheimer's disease pathology through tau and amyloid-β protein propagation. This study investigates prion strain diversity and selective vulnerability patte","entities":{"genes":["HSP90AA1/MAP6/SNAP25"],"diseases":["Alzheimer's Disease"]},"model_system":"mouse","_schema_version":1,"experiment_type":"clinical","primary_outcome":"Validate Prion Strain Diversity and Selective Vulnerability","methodology_notes":"Phase 1 (Weeks 1-2): Prepare transgenic mice (n=60 per strain group, 3-4 months old) expressing human tau and APP. Acclimate animals and perform baseline cognitive testing using Morris water maze and Y-maze. Phase 2 (Week 3): Intracerebral inoculation of prion strains - 22L, ME7, RML strains (20μL, 10^6 ID50 units) via stereotactic injection into hippocampus. Control groups receive PBS injection. Phase 3 (Weeks 4-20): Monthly behavioral assessments including rotarod performance, open field activity, and cognitive testing. Collect blood samples biweekly for RT-QuIC analysis of circulating prion seeds. Phase 4 (Weeks 21-40): Sacrifice subgroups (n=10 per timepoint) at 21, 28, 35, and 40 weeks post-inoculation. Perform transcardial perfusion with 4% paraformaldehyde. Phase 5 (Weeks 41-44): Tissue processing and analysis - brain sectioning for immunohistochemistry (PrP, tau, Aβ antibodies), RT-QuIC assays on brain homogenates, Western blot analysis for protein aggregation, and stereologica","replication_status":"single_study","extraction_metadata":{"backfill_at":"2026-04-16T01:00:16.899029","needs_review":true,"extraction_notes":"Backfilled from wiki source (no PMID 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