disease 1,422 words KG: ent-dise-206cda11
kind:diseasesection:diseasesstate:publishedtopic:neurodevelopmental-epilepsy
Contents

Dravet Syndrome

Disease Info
Prevalence1:15,700–40,000 live births
Incidence~1:20,000–50,000 (varies by region)
Sex ratioSlight male predominance (1.5:1)
Family recurrence<5% (mostly de novo variants)
Mutational origin~80% de novo, ~20% inherited from affected or mosaic parent
DatabasesOMIMOrphanetClinicalTrialsPubMed

Knowledge Graph