diseases 1,074 words KG: ent-dise-46e1344e 2026-03-23
kind:diseasessection:diseasesstate:published
Contents

Progressive External Ophthalmoplegia

Disease Info
PrevalenceApproximately 1 in 100,000 individuals
InheritanceCan be autosomal dominant or sporadic
Age of onsetTypically 18-40 years
GenderAffects both males and females equally
Ragged-red fibersAccumulation of abnormal mitochondria
Exercise intoleranceFatigue with minimal exertion
MyopathyProximal muscle weakness
DatabasesOMIMOrphanetClinicalTrialsPubMed

Knowledge Graph