disease 1,457 words KG: cerebral-metabolism-perfusion-cbs
Contents

cerebral-metabolism-perfusion-cbs

Disease Info
Superior parietal lobule hypometabolismAssociated with cortical sensory loss and visuospatial dysfunction
Basal ganglia hypometabolismParticularly in the **putamen** and **globus pallidus**
Primary motor cortex sparingRelative preservation compared to premotor regions, unless disease is advanced[^niethammer2020]
Degree of asymmetryTypically 20-40% difference between hemispheres
Clinical correlationGreater asymmetry correlates with more severe asymmetric motor symptoms
ProgressionAsymmetry tends to persist but may become more bilateral over time
Diagnostic valueHigh specificity (>85%) for distinguishing CBS from PSP
Asymmetric cortical hypoperfusionSimilar pattern to hypometabolism but more sensitive to subtle changes
Basal ganglia hypoperfusionOften more pronounced than metabolic changes
Perfusion-motor cortex dissociationRelative preservation of primary motor cortex perfusion despite motor symptoms[^podgorski2021]
Correlation with clinical featuresPerfusion deficits correlate with specific symptom profiles
KG Connections1 knowledge graph edges
DatabasesOMIMOrphanetClinicalTrialsPubMed

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