disease 3,021 words KG: ent-dise-5e2ffbc1 2026-03-24
kind:diseasesection:diseasesstate:published
Contents

Variant Creutzfeldt-Jakob Disease (vCJD)

Disease Info
ContaminationNeural tissue from infected cattle entered the food chain
Risk materialsBrain, spinal cord, and other neural tissues are most infectious
Meat productsBurgers, sausages, and other processed meats posed higher risk
CookingNormal cooking does not inactivate the prion
Species barrierUsually prevents efficient transmission between species
BSE to humansThe BSE prion was able to infect humans efficiently
Genetic factorsPRNP polymorphisms may influence susceptibility
DosingMassive exposure in the food supply overcame the barrier
VariabilityRanges from 5 to over 30 years
Exposure timingMost cases likely exposed in the late 1980s or early 1990s
GeneticsPRNP 129 genotype influences incubation period
Future casesIndividuals exposed may develop disease for decades
DatabasesOMIMOrphanetClinicalTrialsPubMed

Knowledge Graph