disease 3,156 words KG: ent-dise-47a28a7f 2026-03-24
kind:diseasesection:diseasesstate:publishedevidence:strong
Contents

Neuroacanthocytosis Syndromes

Disease Info
Vesicle traffickingVPS13 proteins are involved in intracellular membrane transport between organelles[@du2020]
Cytoskeletal organizationChorein may interact with the actin cytoskeleton and affect membrane protein distribution[@velayosbaeza2004]
AutophagyImpaired autophagic flux may lead to accumulation of damaged organelles and proteins[@zhang2020]
Iron metabolismAltered iron handling may contribute to oxidative stress and neuronal injury[@mazarati2021]
Mitochondrial dysfunctionImpaired energy metabolism and increased oxidative stress[@hara2014]
Dysregulated iron metabolismElevated ferritin levels and iron accumulation in the basal ganglia[@kawai2007]
ExcitotoxicityEnhanced glutamatergic signaling leading to calcium overload[@danek2009]
Peripheral neuropathyDemyelinating neuropathy with loss of proprioception and reflexes[@koren2015]
AtaxiaCerebellar degeneration leading to gait instability[@harding1991]
Retinitis pigmentosaProgressive photoreceptor degeneration[@runge1986]
DystoniaSustained or intermittent muscle contractions causing abnormal postures or movements[@bader2011a]
TremorRhythmic oscillatory movements, typically rest or action tremor[@vitale2016]
DatabasesOMIMOrphanetClinicalTrialsPubMed

Knowledge Graph