| Prevalence | 2-3 cases per million per year for PACNS |
| Prognosis | Potentially reversible with treatment if caught early |
| Systemic vasculitides | Giant cell arteritis, Takayasu arteritis, polyarteritis nodosa |
| Infection-associated | Syphilis, Lyme disease, viral vasculitis |
| Autoimmune-associated | SLE, Behçet's disease, sarcoidosis |
| Drug-induced | Cocaine, amphetamines, certain medications |
| Small vessel vasculitis | Lenticulostriate arteries, thalamoperforating arteries |
| Medium vessel vasculitis | Cortical arteries, penetrating branches |
| Large vessel vasculitis | Internal carotid, vertebral, basilar arteries |
| Progressive cognitive decline | Often subacute onset over weeks to months |
| Executive dysfunction | Planning, organization, problem-solving difficulties |
| Memory impairment | Both short-term and working memory |
| Databases | OMIMOrphanetClinicalTrialsPubMed |