disease 1,759 words KG: ent-dise-9a1d57a2 2026-03-24
kind:diseasesection:diseasesstate:published
Contents

Myelin Oligodendrocyte Glycoprotein Antibody-Associated Disease (MOGAD)

Disease Info
Prevalence1-5 per 100,000 population 3
Incidence0.5-2 per million per year
Age distributionBimodal—peaks in childhood (median: 7 years) and adulthood (median: 35 years)
Gender distributionMore common in males in childhood; female predominance in adults
EthnicityNo strong ethnic predominance, unlike NMOSD
FunctionCell adhesion molecule, involved in:
ExpressionOligodendrocyte surface, myelin sheaths
ImmunogenicityHighly species-conserved, targets for demyelinating antibodies
IsotypePredominantly IgG1 (can fix complement)
TargetConformational epitopes on extracellular domain of MOG
Primary oligodendrocyte injuryDirect demyelination
Less complement activationMOG antibodies are less potent activators
DatabasesOMIMOrphanetClinicalTrialsPubMed

Knowledge Graph