| Prevalence | nfvPPA accounts for approximately 25-30% of all PPA cases |
| Age of onset | Typically between 50-70 years, with a mean onset age of 65 years |
| Sex distribution | Slight male predominance in some cohorts |
| Family history | 30-50% have affected first-degree relatives |
| Disease duration | Typically 8-15 years from symptom onset to death |
| Dysarthria | Slurred speech due to impaired muscle control |
| Articulatory groping | Visible effort to produce sounds |
| Involuntary repetitions | Palilalia (repetition of one's own sounds/words) |
| Prosodic deficits | Abnormal rhythm, stress, and intonation patterns |
| Parkinsonism | Particularly in cases with underlying Corticobasal Degeneration |
| Behavioral changes | Apathy, disinhibition (less prominent than in bvFTD) |
| Memory impairment | Usually develops later than in typical Alzheimer's |
| Databases | OMIMOrphanetClinicalTrialsPubMed |
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