protein 673 words KG: ALPHAGALACTOSIDASEA
Contents

Alpha-Galactosidase A Protein

🔬 Protein Info
Gene SymbolALPHAGALACTOSIDASEA
AliasesALPHAGALACTOSIDASEA
Subcellular Localization** | Lysosome |
Primary structure429 amino acids (including signal peptide)
Processed form398 amino acids (after signal peptide removal)
QuaternaryHomodimer
GlycosylationN-linked glycans at positions 108, 146, 192
Catalytic residuesAsp170, Asp231 (acid/base catalysts)
Substrate bindingHydrophobic pocket for globotriaosylceramide
SpecificityTerminal α-galactosyl residues
Glycolipid catabolismPrevents accumulation of GL-3
Membrane turnoverProcesses glycolipids from aging membranes
Renal functionCritical for glomerular and tubular cells
Vascular functionPrevents endothelial glycolipid accumulation
DatabasesGeneCardsUniProtNCBI GeneHPASTRING

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UniProtWikipedia

Related Hypotheses (3)

Heat Shock Protein 70 Disaggregase Amplification
Score: 0.62
Serine/Arginine-Rich Protein Kinase Modulation
Score: 0.62
Designer TRAK1-KIF5 fusion proteins accelerate therapeutic m
Score: 0.62

Related Analyses (7)

Mitochondrial transfer between astrocytes and neurons
neurodegeneration · archived
Protein aggregation cross-seeding across neurodegenerative d
neurodegeneration · completed
GBA-Synuclein Loop Therapeutics for PD
neurodegeneration · completed
RNA binding protein dysregulation across ALS FTD and AD
neurodegeneration · archived
RNA binding protein dysregulation across ALS FTD and AD
neurodegeneration · completed

Related Experiments (13)

Animal Model Comparison for Neurodegenerative Disease Therap
clinical · proposed · Score: 0.40
Endocannabinoid System Dysfunction Validation in Parkinson's
clinical · proposed · Score: 0.40
Glymphatic-Circadian Axis Enhancement Therapy for Parkinson'
clinical · proposed · Score: 0.40
Cytochrome Therapeutics
clinical · proposed · Score: 0.40
Gut Microbiome-Derived Metabolites in Alpha-Synuclein Propag
clinical · proposed · Score: 0.40

See Also (1)

Neurodegeneration
disease · KG edge: implicated_in

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