disease 3,312 words KG: ent-dise-93aac149 2026-03-24
kind:diseasesection:diseasesstate:published
Contents

Shy-Drager Syndrome

Disease Info
1960Milton Shy and Glenda Drager described a syndrome of autonomic failure with parkinsonism[@shy1960a]
1969The term "Shy-Drager syndrome" came into common use following detailed clinical descriptions[@bannister1972]
1989Multiple system atrophy (MSA) was proposed as an umbrella term encompassing Shy-Drager syndrome, striatonigral degeneration, and olivopontocerebellar atrophy[@graham1989]
1998Discovery of α-synuclein in glial cytoplasmic inclusions established the proteinaceous basis of MSA[@spillantini1997]
2008Second consensus criteria for MSA established modern diagnostic framework[@gilman2008]
DatabasesOMIMOrphanetClinicalTrialsPubMed

Knowledge Graph

Related Hypotheses (1)

Blocking AGE-RAGE Signaling in Enteric Glia to Prevent Neuro
Score: 0.42

Related Analyses (29)

4R-tau strain-specific spreading patterns in PSP vs CBD
neurodegeneration · archived
Astrocyte reactivity subtypes in neurodegeneration
neurodegeneration · archived
Blood-brain barrier transport mechanisms for antibody therap
neurodegeneration · archived
Microglia-astrocyte crosstalk amplification loops in neurode
neurodegeneration · archived
Autophagy-lysosome pathway convergence across neurodegenerat
neurodegeneration · archived

Related Experiments (6)

ER-Golgi Secretory Pathway Dysfunction in PD - Experiment De
clinical · proposed · Score: 0.40
cGAS-STING Pathway Validation Study in Parkinson's Disease
clinical · proposed · Score: 0.40
Epigenetic Dysregulation Validation in Parkinson's Disease
clinical · proposed · Score: 0.40
Iron Dyshomeostasis in MSA Pathogenesis Experiment
validation · proposed · Score: 0.40
Non-Motor Symptom Progression in Parkinson's Disease — Mecha
clinical · proposed · Score: 0.40