entity 1,096 words KG: ent-gene-803bc7b7 2026-03-24
kind:entitysection:entitiesstate:published
Contents

ATP7B Gene

🔬 Protein Info
Gene SymbolATP7B
Chromosome13q14.3.
Functionis an important component in the neurobiology of neurodegenerative diseases.
Primary Expressionhepatocytes, where it [@czonkowska2018] supports both copper incorporation into ceruloplasmin and biliary copper excretion
Subcellular Localizationand protein-protein interactions
Molecular Weight165 kDa
Amino Acids1465 aa
Exons21
GeneCardsATP7B
Human Protein AtlasATP7B
N-terminal metal-binding domainContains six tandem copper-binding repeats (CBD1-CBD6) that sequester excess copper
Transmembrane architectureEight core transmembrane domains forming the ion-transporting channel
P-domainCatalytic phosphorylation site characteristic of P-type ATPases
A-domainAdenosine nucleotide-binding domain essential for ATP hydrolysis
C-terminal tailContains targeting signals for subcellular localization and protein-protein interactions
Associated DiseasesAging, Als, Alzheimer, Amyotrophic Lateral Sclerosis, Ataxia, Cirrhosis
InteractionsCP
KG Connections23 knowledge graph edges
DatabasesGeneCardsUniProtNCBI GeneHPASTRING

Knowledge Graph