🧫

Gabra1+/-/Gabrg2+/- mouse model characterization

experiment Created: 2026-04-10 14:39:20 By: experiment_extractor Quality: 90% ✓ SciDEX ID: experiment-exp-e625043d-a37c-457e-971e-7
🧫 Experiment Protocol Animal Model
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Related Entities
Gabra1, Gabrg2
Metadata
experiment_typeanimal_model
protocolEEG monitoring, electroretinography, visual evoked potentials, electron microscopy, immunohistochemistry
expected_outcomesSpontaneous seizures, reduced GABAA receptor expression, optic nerve degeneration
success_criteriaRecapitulation of human phenotype
sample_sizeNone
statistical_methodsNone
p_valueNone
effect_sizeNone
extracted_at2026-04-10T07:39:20.599994
source_pmid37703949
_origin{'type': 'internal', 'url': None, 'tracked_at': '2026-04-10T14:39:20.631540'}
🌍 Provenance Graph 2 nodes, 1 edges

derives from (1)

Linked Artifacts (18)
derives_from📄Epilepsy plus blindness in microdeletion of GABRA1 and GABRG100%
related🧫Optic nerve myelination analysis100%
related🧫Phenobarbital treatment efficacy study100%
related🧫Clinical characterization of GABRA1/GABRG2 microdeletion pat100%
mentions📖GABRA1 Gene80%
mentions📖GABRA1 Protein80%
mentions📖GABRG2 — GABA-A Receptor Gamma2 Subunit80%
mentions📖GABRG2 Protein — GABA-A Receptor Gamma2 Subunit80%
related📖GABRA1 Gene72%
related📖GABRA1 Protein72%
related📖GABRG2 — GABA-A Receptor Gamma2 Subunit72%
related📖GABRG2 Protein — GABA-A Receptor Gamma2 Subunit72%
mentions📖brain-regions60%
mentions📖Epilepsy60%
related📖Epilepsy60%
related📖brain-regions54%
related📖Epilepsy54%
mentions📖GABA-A Gamma2 Neurons50%