mechanism 1,662 words KG: ent-gene-2488b5f0 2026-03-24
kind:mechanismsection:mechanismsstate:published
Contents

SOD1 ALS Pathway

🔬 Protein Info
Gene Symbolent-gene-2488b5f0
Destabilized dimer interfaceMutations weaken SOD1 dimer stability
Reduced metal bindingLoss of zinc/copper cofactors increases aggregation
Increased hydrophobic exposurePromotes oligomerization and aggregation
Post-translational modificationsOxidation, nitration accelerate aggregation
Direct bindingMutant SOD1 binds to mitochondria
Complex I inhibitionReduced ATP production
Calcium handlingImpaired mitochondrial calcium buffering
Drp1 dysregulationAbnormal mitochondrial fission
ApoptosisCytochrome c release, caspase activation
KG Connections2 knowledge graph edges
DatabasesGeneCardsUniProtNCBI GeneHPASTRING

Knowledge Graph

Related Hypotheses (27)

Bacterial Enzyme-Mediated Dopamine Precursor Synthesis
Score: 0.36
Multiplexed Base Editing for Simultaneous Neuroprotective Ge
Score: 0.53
Acid-Degradable LNP-Mediated Prenatal CRISPR Intervention fo
Score: 0.47
TREM2-mediated microglial tau clearance enhancement
Score: 0.49
TREM2 Conformational Stabilizers for Synaptic Discrimination
Score: 0.41

Related Analyses (30)

CRISPR-based therapeutic approaches for neurodegenerative di
neurodegeneration · completed
TDP-43 phase separation therapeutics for ALS-FTD
neurodegeneration · archived
RNA binding protein dysregulation across ALS FTD and AD
neurodegeneration · archived
CRISPR-based therapeutic approaches for neurodegenerative di
neurodegeneration · archived
Microglial subtypes in neurodegeneration — friend vs foe
neuroscience · failed

Related Experiments (23)

s:** - Temporal analysis showing mitochondrial defects prece
falsification · proposed · Score: 0.40
s:** - Single-cell RNA-seq to measure editing efficiency acr
falsification · proposed · Score: 0.40
ALS Regional Onset and Spread: Network-Level Staging Model
clinical · proposed · Score: 0.40
Viral and Post-Infectious Mechanisms in ALS — Experiment Des
clinical · proposed · Score: 0.40
Metabolic Pathway-Targeted Therapy in ALS
clinical · proposed · Score: 0.40

Knowledge Graph (2 edges)

ent-gene-2488b5f0 data_in benchmark_ot_ad_answer_key:SOD1
benchmark_ot_ad_answer_key:SOD1 data_in ent-gene-2488b5f0