mechanism 1,662 words KG: ent-gene-2488b5f0
Contents

SOD1 ALS Pathway

🔬 Protein Info
Gene Symbolent-gene-2488b5f0
Destabilized dimer interfaceMutations weaken SOD1 dimer stability
Reduced metal bindingLoss of zinc/copper cofactors increases aggregation
Increased hydrophobic exposurePromotes oligomerization and aggregation
Post-translational modificationsOxidation, nitration accelerate aggregation
Direct bindingMutant SOD1 binds to mitochondria
Complex I inhibitionReduced ATP production
Calcium handlingImpaired mitochondrial calcium buffering
Drp1 dysregulationAbnormal mitochondrial fission
ApoptosisCytochrome c release, caspase activation
Aberrant peroxidase activityMutant SOD1 can use substrates improperly
Nitric oxide interactionForms peroxynitrite
Lipid peroxidationMembrane damage
DNA damage8-OHdG accumulation
Reduced glutamate transportEAAT2 downregulation
AMPA receptor dysregulationCalcium-permeable AMPA receptors
KG Connections2 knowledge graph edges
DatabasesGeneCardsUniProtNCBI GeneHPASTRING

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pg 1/2Next →

Related Analyses (30)

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neurodegeneration · completed
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Related Experiments (23)

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Knowledge Graph (2 edges)

ent-gene-2488b5f0 data_in benchmark_ot_ad_answer_key:SOD1
benchmark_ot_ad_answer_key:SOD1 data_in ent-gene-2488b5f0

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