mechanism 2,648 words KG: ent-gene-28e2cb01 2026-03-24
kind:mechanismsection:mechanismsstate:published
Contents

TREM2 in ALS

🔬 Protein Info
Gene Symbolent-gene-28e2cb01
PhagocytosisTREM2 signaling enhances clearance of debris, apoptotic cells, and protein aggregates
Cytokine regulationModulates production of inflammatory cytokines including IL-6, TNF-α, and IL-1β
Metabolic adaptationSupports microglial lipid metabolism and mitochondrial function
Cell survivalProvides pro-survival signaling through AKT activation
[TREM2](/genes/trem2) variantsWhile TREM2 R47H is strongly associated with AD risk, evidence for ALS is weaker
[TYROBP](/genes/tyrobp)Genetic variants in the TREM2 signaling adaptor show nominal association with ALS
Gene expressionSingle-cell RNA-seq studies show altered TREM2 expression in ALS microglia
TREM2 knockout miceShow altered microglial responses in ALS models
TREM2 agonismPreclinical studies suggest TREM2-activating antibodies may enhance neuroprotection
C9orf72 connectionThe C9orf72 gene (most common ALS cause) regulates lysosomal function, potentially linking to TREM2-mediated phagocytosis
TimingOptimal intervention window (presymptomatic vs. symptomatic) unclear
Biomarker needNo validated biomarkers for TREM2 pathway activity in ALS patients
Safety concernsOver-activation could exacerbate neuroinflammation
Patient selectionWhich ALS subtypes would benefit most from TREM2-targeted therapy
KG Connections5 knowledge graph edges
DatabasesGeneCardsUniProtNCBI GeneHPASTRING

Knowledge Graph

Related Hypotheses (30)

TREM2-Dependent Astrocyte-Microglia Cross-talk in Neurodegen
Score: 0.64
TREM2-Mediated Astrocyte-Microglia Cross-Talk in Neurodegene
Score: 0.61
TREM2-Mediated Astrocyte-Microglia Crosstalk in Neurodegener
Score: 0.61
TREM2-CSF1R Cross-Talk in Microglial Metabolic Reprogramming
Score: 0.59
TREM2-SIRT1 Metabolic Senescence Circuit in Microglial Aging
Score: 0.59

Related Analyses (30)

Immune atlas neuroinflammation analysis in neurodegeneration
Neuroinflammation · completed
Neuroinflammation and microglial priming in early Alzheimer'
neurodegeneration · archived
Neuroinflammation and microglial priming in early AD
neurodegeneration · completed
TREM2 Therapeutic Strategy Post-INVOKE-2
neurodegeneration · archived
Mechanistic validation of SEA-AD differential expression hyp
neurodegeneration · failed

Related Experiments (30)

TREM2 KO amyloid pathology study
validation · completed · Score: 0.75
TREM2 KO amyloid pathology study
validation · completed · Score: 0.75
TREM2 KO amyloid pathology study
validation · in_progress · Score: 0.75
TREM2 KO amyloid pathology study
validation · completed · Score: 0.75
TREM2 KO amyloid pathology study
validation · completed · Score: 0.75

See Also (7)

TREM2 Gene-Mechanism-Therapy Chain — From Genetic Risk
mechanism · Pages share 3 hypotheses
TREM2 in Frontotemporal Dementia
mechanism · Pages share 3 hypotheses
TREM2 in Amyotrophic Lateral Sclerosis
mechanism · Pages share 3 hypotheses
TREM2 Gene
gene · Pages share 3 hypotheses
al002-trem2-agonist-alzheimers
clinical_trial · Pages share 3 hypotheses

Knowledge Graph (5 edges)

ent-gene-28e2cb01 expressed_in microglia
ent-gene-28e2cb01 data_in ad_genetic_risk_loci:TREM2
ent-gene-28e2cb01 data_in benchmark_ot_ad_answer_key:TREM2
ad_genetic_risk_loci:TREM2 data_in ent-gene-28e2cb01
benchmark_ot_ad_answer_key:TREM2 data_in ent-gene-28e2cb01