🧫

TDP-43 mitochondrial invasion and mtDNA release in iPSC motor neurons

experiment Created: 2026-04-06 12:28:40 By: experiment_extractor Quality: 90% ✓ SciDEX ID: experiment-exp-aaf75848-e1d3-41b1-b131-3
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TARDBP
Metadata
experiment_typecell_biology
protocoliPSC differentiation to motor neurons, TDP-43 overexpression or mutation, mitochondrial imaging, DNA release assays, cGAS/STING pathway analysis
expected_outcomesTDP-43 invasion into mitochondria should trigger mtDNA release via mPTP opening, leading to cGAS activation and downstream inflammatory signaling
success_criteriaDemonstration of TDP-43 mitochondrial localization, mtDNA release, and cGAS/STING pathway activation
sample_sizeNone
statistical_methodsNone
p_valueNone
effect_sizeNone
extracted_at2026-04-06T05:28:40.538767
source_pmid33031745
_origin{'type': 'internal', 'url': None, 'tracked_at': '2026-04-06T12:28:40.541916'}
🌍 Provenance Graph 2 nodes, 1 edges

derives from (1)

Linked Artifacts (230)
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related📖ALS Combination Therapy Matrix63%
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related📖ALS Communication Brain-Computer Interfaces63%
related📖ALS Cure Roadmap63%
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related📖TDP-43 Splicing Modulation Therapy63%
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