protein 1,180 words KG: TSC1PROTEIN 2026-03-28
kind:proteinsection:proteinsstate:publishedrole:tumor-suppressor
Contents

TSC1 Protein — Hamartin

🔬 Protein Info
Gene SymbolTSC1
Full NameTuberous Sclerosis Complex 1
AliasesTSC1, Hamartin, KCAA0025
Protein FamilyTSC family
FunctionIt contains several functional domains including a hamartin elbow domain (HED), a transmembrane region, and a conserved tuberous sclerosis complex domain (TSC-TBD)[1].
Primary Expressionneurons and plays important roles in synaptic plasticity, dendritic spine morphology, and neuronal connectivity
Subcellular LocalizationCytoplasm, lysosomes, endosomes
Molecular Weight~130 kDa (1164 amino acids)
Amino Acids164 aa
PathwaysmTOR Signaling, mTOR, mtor
UniProt IDQ9UMX0
Ensembl IDENSG00000115159
GeneCardsTSC1
Human Protein AtlasTSC1
Protein NameHamartin (TSC1)
Associated DiseasesAging, Als, Cardiovascular, Ms, Tuberous sclerosis complex, epilepsy
Known Drugs/Compoundsrapamycin
InteractionsMTOR, TSC2, AKT, FIP200, AKT3, PIK3CA
KG Connections212 knowledge graph edges
DatabasesGeneCardsNCBI GeneHPASTRING

Knowledge Graph