cell 700 words KG: ent-gene-5b8aa21c 2026-03-24
kind:cell-typesection:cell-typesstate:published
Contents

PSEN1-Mutant Neurons

🔬 Protein Info
Gene SymbolPSEN1
Full NameMutant Neurons
Chromosome14q24.2
Protein TypeAspartyl protease (catalytic subunit)
Functionβ-Secretase Cleavage: APP is first cleaved by BACE1 to generate C99 (membrane-bound C-terminal fragment)
Molecular Weight27 kDa
Amino Acids467 aa
PathwaysAmyloid, Autophagy, Blood-Brain Barrier, Cholesterol, Dysbiosis
UniProt IDP49768
NCBI Gene ID5663
GeneCardsPSEN1
Human Protein AtlasPSEN1
Altered Aβ productionMost PSEN1 mutations shift the gamma-secretase cleavage pattern toward generating more aggregation-prone Aβ42 and Aβ43 species
Reduced Aβ40 productionSome mutations decrease the production of the shorter, less toxic Aβ40
Aβ42/40 ratio increaseThe increased ratio of Aβ42 to Aβ40 is believed to accelerate amyloid plaque formation
Associated DiseasesAD, ALS, ALZHEIMER, AMI, Aging
Known Drugs/CompoundsRAPAMYCIN, rapamycin
InteractionsDAPK1, HSPG2, IL1B, APP, EIF2AK2, CD33
KG Connections1522 knowledge graph edges
DatabasesGeneCardsHPASTRING

Knowledge Graph

Related Hypotheses (5)

Synthetic Biology BBB Endothelial Cell Reprogramming
Score: 0.57
Senescent Cell Mitochondrial DNA Release
Score: 0.54
Astrocytic Lactate Shuttle Enhancement for Grid Cell Bioener
Score: 0.41
Grid Cell-Specific Metabolic Reprogramming via IDH2 Enhancem
Score: 0.38
Age-Dependent Complement C4b Upregulation Drives Synaptic Vu
Score: 0.47

Related Analyses (11)

Selective vulnerability of entorhinal cortex layer II neuron
neurodegeneration · archived
Blood-brain barrier transport mechanisms for antibody therap
neurodegeneration · archived
Senolytic therapy for age-related neurodegeneration
neurodegeneration · archived
Gene expression changes in aging mouse brain predicting neur
neurodegeneration · archived
Mitochondrial transfer between neurons and glia
neurodegeneration · archived

Related Experiments (7)

Creation and validation of 3xAD-ChAT-Cre mouse model
validation · proposed · Score: 0.90
Adoptive transfer of TCRAβ-Tregs in AD mouse model
validation · proposed · Score: 0.90
Behavioral assessment of APP/PSEN1/GD3S triple-mutant mice
validation · proposed · Score: 0.90
Amyloid plaque load analysis in triple-mutant mouse brains
exploratory · proposed · Score: 0.88
Tet2 expression analysis in aged 2×Tg-AD mouse brains
exploratory · proposed · Score: 0.85

Knowledge Graph (4 edges)

ent-gene-5b8aa21c data_in ad_genetic_risk_loci:PSEN1
ent-gene-5b8aa21c data_in benchmark_ot_ad_answer_key:PSEN1
ad_genetic_risk_loci:PSEN1 data_in ent-gene-5b8aa21c
benchmark_ot_ad_answer_key:PSEN1 data_in ent-gene-5b8aa21c