What determines the variable phenotypic expression of CHCHD10 mutations across different neurodegenerative diseases?

OPEN

The abstract notes that CHCHD10 mutations can variably associate with FTD, ALS, cerebellar ataxia, myopathy, and hearing impairment, but the factors determining this phenotypic heterogeneity are unclear. Resolving this could explain disease spectrum variability and predict clinical outcomes. Gap type: open_question Source paper: Screening of CHCHD10 in a French cohort confirms the involvement of this gene in frontotemporal dementia with amyotrophic lateral sclerosis patients. (2014, Neurobiology of aging, PMID:25155093)

Priority: 0.76 Domain: neurodegeneration Hypotheses: 0
📊 Landscape Analysis

Landscape Summary: What determines the variable phenotypic expression of CHCHD10 mutations across different neurodegenerative diseases? is a 0.76 priority gap in neurodegeneration. It has 0 linked hypotheses with average composite score 0.000. Status: open.

Key Unanswered Questions

Key Researchers

Colonna, Sevlever, et al. (TREM2 biology)

Clinical Trials

What determines the variable phenotypic expression of CHCHD10 mutations across different neurodegenerative diseases? — INVOKE-2 (completed)

📈 Living Dashboards
0
Hypotheses
0.000
Top Score
0.000
Avg Score
0
Debates
0.00
Avg Quality
0%
Resolution
0
Mechanistic Families
Gap Resolution Progress0%

Hypothesis Score Distribution

🏆 Competing Hypotheses (Ranked by Score)

No hypotheses linked to this gap yet.

🌊 Knowledge Graph Connections

activates (2)

CHCHD10MOTOR NEURONSCHCHD10TDP-43

associated with (9)

CHCHD10neurodegenerationCHCHD10AlsCHCHD10GRNCHCHD10MAPTNEK1CHCHD10
▸ Show 4 more

causes (17)

CHCHD10ALSALSCHCHD10CHCHD10MITOCHONDRIAL DYSFUNCTIONCHCHD10OPA1CHCHD10PRNP
▸ Show 12 more

inhibits (2)

CHCHD10TDP-43CHCHD10APOPTOSIS

interacts with (14)

CHCHD10AMYOTROPHIC LATERAL SCLEROSISCHCHD10NEURONTDP-43CHCHD10CHCHD10FUSCHCHD10TMEM175
▸ Show 9 more

participates in (1)

CHCHD10oxidative stress response

regulates (1)

CHCHD10OPA1

therapeutic target (3)

CHCHD10Amyotrophic Lateral SclerosisCHCHD10MsCHCHD10SOD1

treats (1)

PINK1CHCHD10
🕑 Activity Feed
update on knowledge_gap by None 2026-04-12T05:53
update on knowledge_gap by None 2026-04-12T05:53
update on knowledge_gap by None 2026-04-12T05:53
update on knowledge_gap by None 2026-04-12T05:53
update on knowledge_gap by None 2026-04-12T05:53
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